Mounier Kuhn Syndrome

Authors

  • Silvio Stomeo

DOI:

https://doi.org/10.1285/i25327518v3i2p27

Keywords:

Tracheobroncomegalia, bronchiectasis, diverticula, clearance, chronic inflammation, atrophy, connective tissue disorders (Ehlers-Danlos syndrome and Marfan syndrome)

Abstract

Mounier Kuhn syndrome or tracheobronchomegaly is characterized by a marked dilatation of the trachea and main bronchi that can extend to the periphery of the lungs. Dilation is due to an alteration of the cartilaginous and membranous structure of the trachea and bronchi. It is a pathology much more frequent in men. The aetiology is unclear. The clinical case in question concerns a 67-year-old man who has reported recurrent episodes of bronchopulmonary infections and hemoptysis, after undergoing instrumental investigations (fibrobroncoscopy and chest CT), the diagnosis of Tracheobroncomegalia or Mounier Kuhn syndrome was formulated.

Downloads

Published

05-05-2020

Issue

Vol. 3, issue 2 (2019)

Section

Articles

License

Authors who publish with this publication accept all the terms and conditions of the Creative Commons license at the link below.

Gli autori che pubblicano in questa rivista accettano i termini e le condizioni specificate nella licenza Creative Commons di cui al link sottostante.

https://creativecommons.org/licenses/by-nc-nd/3.0/it/legalcode